论文部分内容阅读
角膜格子样营养不良常在10岁时发现。其特殊改变曾早在2岁迟在30-40岁时被查到。约在20岁时肉眼明显可见典型的病害。本病特征是角膜中央区基质浅层内有线状混浊,上皮一般不受损害。所以在30-40岁之前一直能保持好的视力。病变严重时角膜敏感度减退,但病变周围的基质一直到晚年仍保持透明。角膜混浊最后可融合成一灰白色中央角膜白斑。本病是常染色体显性遗传。单侧角膜营养不良罕见,亦未报导过有家族史的病例。本文叙述了一个家族中5例单侧及1例双侧
Corneal trellis malnutrition often found at the age of 10. Its special changes were found as late as 2 years old 30-40 years old. About 20 years of age when the naked eye can clearly see the typical disease. The disease is characterized by a linear matrix opacity in the central corneal stroma, the epithelium is generally not damaged. So 30-40 years old has been able to maintain good eyesight. Corneal sensitivity decreased when the lesion was severe, but the stroma surrounding the lesion remained clear until later years. Corneal opacity can finally be fused into an off-white central cornea. The disease is autosomal dominant. Unilateral corneal dystrophy rare, nor reported cases of family history. This article describes a family of 5 cases of unilateral and 1 bilateral