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目的：总结分析1984～1996年在我院经病理证实的眶内原发性横纹肌肉瘤。方法：回顾研究11例眶内横纹肌肉瘤的临床特点、影像诊断、治疗方法及预后。结果：原发性眶内横纹肌肉瘤多发生在10岁以下儿童，起病急、发展较快，常以进行性眼球突出就诊，可伴有眼部红肿、眼球运动受限等改变。影像检查本瘤形态多为类圆形或不规则形，内回声较低，图像欠均匀，可伴骨破坏以及动态观察肿瘤不断生长等特点，可根示肿瘤的性质。经手术联合放疗及化疗等综合治疗手段，疗效满意，7例随访者中5例存活3～12年，2例已观察1年半及9个月，未见复发。结论：横纹肌肉瘤是儿童时期眼眶恶性肿瘤中治疗效果最佳的肿瘤，影像检查有其特点，采用综合疗法，可大大提高患者的存活率。
Objective: To summarize and analyze the primary orbital primary rhabdomyosarcoma confirmed by pathology in our hospital from 1984 to 1996. Methods: The clinical features, imaging diagnosis, treatment and prognosis of 11 cases of orbital rhabdomyosarcoma were retrospectively studied. Results: Primary orbital rhabdomyosarcoma occurred in children under 10 years of age, the onset of acute and rapid development, often with prominent eye treatment, may be associated with eye swelling, limited eye movement and other changes. Image examination of the tumor morphology mostly round or irregular shape, lower echo, the image is not uniform, with bone destruction and dynamic observation of tumor growth and other characteristics, can be rooted in the nature of the tumor. After the operation combined with radiotherapy and chemotherapy and other comprehensive treatment, the curative effect was satisfactory. Among the 7 follow-up cases, 5 cases survived for 3 to 12 years. Two cases had been observed for 1 year and a half months and 9 months without recurrence. Conclusion: Rhabdomyosarcoma is the most effective tumor in the treatment of orbital malignant tumors in childhood. The imaging examination has its own characteristics. The comprehensive therapy can greatly improve the survival rate of patients.