论文部分内容阅读
目的总结复发性腹膜后恶性纤维组织细胞瘤的诊治经验。方法回顾性分析1990~ 2 0 0 2年收治的 2 9例复发性腹膜后恶性纤维组织细胞瘤的临床与病理资料。结果 12例(4 1 4 % )患者在首次复发时完整切除肿瘤 ;有 7例患者分别在首次 (2例 )、2次 (3例 )和 3次 (2例 )复发时进行联合脏器切除。对 2 5例患者进行 6个月至 8年的随访 ,1、3年及 5年以上生存率分别为73 2 %、4 6 7%和 19 8%。结论外科手术切除肿瘤是提高复发性腹膜后恶性纤维组织细胞瘤生存率最重要的手段 ,联合脏器切除能提高肿瘤完整切除率。
Objective To summarize the diagnosis and treatment of recurrent retroperitoneal malignant fibrous histiocytoma. Methods The clinical and pathological data of 29 patients with recurrent retroperitoneal malignant fibrous histiocytoma from 1990 to 2002 were retrospectively analyzed. Results Twenty-four patients (14.4%) underwent complete resection of the tumor at the first relapse. Seven patients underwent combined organ resection at the first (2), 2 (3) and 3 (2) . Follow-up was performed in 25 patients from 6 months to 8 years. The survival rates were 73 2%, 467% and 19 8% after 1, 3 and 5 years respectively. Conclusion Surgical resection of the tumor is the most important means to improve the survival rate of recurrent retroperitoneal malignant fibrous histiocytoma. Combined resection of the organ can improve the complete resection rate of the tumor.