1961年,Gass 首先应用了“急性后部的多灶性鳞状(Placoid)色素上皮病变”这一名称,描述了患此病的三名妇女。由于后来的病例报告,它被接受作为一个临床疾病。日益增多的实验指出,病理学的改变除累及色素上皮层外,可以侵犯眼内其他组织。本文作者报告了一例具有视乳头水肿的鳞状色素上皮病变的患者。19岁。于1972年8月间,左右眼相继发病,眼底改变相似:典型的、白色的、局限性的视网膜病损和鳞状色素上皮病变的不规则的色素改变,累及整个后极部。视乳头充血及轻度模糊,但不高起。荧光血管造影证实为本病的典型表现,但无视乳头的荧光过多。同年12月,头部遭受外伤,颅骨X 片没有发现骨折。1973年1月查体时发现双侧视乳头水肿,为立体镜裂隙灯所证实。其余的神 In 1961 Gass first applied the name “acute rear multiplayer lesions of the plaque epithelium”, describing three women with the disease. As a result of later case reports, it was accepted as a clinical disease. An increasing number of experiments indicate that pathological changes can involve other tissues in the eye, in addition to involving the pigment epithelium. The authors report a case of squamous pigmented epithelial lesions with papilledema. 19 years old. In August 1972, both the left and right eyes developed one after another, with similar fundus changes: an irregular, pigmentary change in the typical, white, localized retinopathy and squamous pigmented epithelial lesions involving the entire posterior pole. Optic congestion and mild blur, but not high. Fluorescent angiography confirmed the typical manifestation of this disease, but ignored the nipple’s hyperpigmentation. In the same year in December, the head suffered trauma, skull X-ray found no fracture. Bilateral papillary edema was found on examination in January 1973 and was confirmed by a stereoscopic slit lamp. The rest of God