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1975~1987年我院共诊治头颈部横纹肌肉瘤(RMS)23例,占全身各部RMS的44.2%。原发部位以中耳、颞、颊、上颌、下颌较多见。病理类型依次为胚胎型、腺泡型、葡萄簇型和多形型。治疗采用单纯手术、放疗或化疗,或2~3种治疗方法联合应用。死亡10例,存活8例,失访5例。预后直接与病变部位、范围及程度有关。提示,为提高本病的生存率,应早期诊断,早期采用多种治疗方法联合治疗。
From 1975 to 1987, 23 cases of rhabdomyosarcoma of the head and neck (RMS) were diagnosed and treated in our hospital, accounting for 44.2% of the RMS of the whole body. The primary site was more common in the middle ear, chin, cheek, upper jaw, and lower jaw. Pathological types were embryonic, acinic, grape cluster, and polymorphic. Treatments were performed with simple surgery, radiotherapy or chemotherapy, or a combination of 2 or 3 treatments. There were 10 deaths, 8 cases survived, and 5 cases lost to follow-up. The prognosis is directly related to the location, extent and extent of the lesion. It is suggested that in order to improve the survival rate of the disease, early diagnosis should be made and multiple treatment methods combined for early treatment.