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Garcin1926年首次报告本病;1927年又系统地提出本病特征:一、单侧全部颅神经麻痹;二、无四肢运动及知觉障碍;三、无视神经乳头水肿等颅压增高现象;四、X线摄片颅底有病损改变。此病多见于鼻窦、鼻咽腔及颅底恶性肿瘤晚期,肿瘤破坏了颅底骨质并使单侧颅神经受损。肿瘤从破裂孔进入颅内向前、后侵犯,向前侵犯颅神经麻痹的先后次序为:Ⅴ、Ⅺ、Ⅲ、Ⅳ、Ⅱ、Ⅰ;向后侵犯麻痹的次序为:Ⅸ、Ⅹ、Ⅺ、Ⅷ、Ⅻ、Ⅻ。一般前组颅神经麻痹早于后组。著者报告1例筛窦蝶窦扁平上皮癌合并Gar—cin综合症、并作了屍检。
Garcin first reported the disease in 1926; in 1927 it systematically proposed the characteristics of the disease: 1. All cranial nerve palsy; 2. No limb movements and perceptual disturbances; 3. Absence of increased intracranial pressure, such as papilledema; The radiography changes the lesions at the base of the skull. The disease is more common in the late sinus, nasopharyngeal and skull base malignant tumors, tumor destruction of the skull base and unilateral cranial nerve damage. The tumor enters the skull from the rupture hole forward and then invades. The sequence of the forward violation of cranial nerve palsy is: V, XI, III, IV, II, I; the sequence of backward violation of paralysis is: IX, X, XI, VIII , XII, XII. General precranial nerve palsy was earlier than the posterior group. The authors reported one case of ethmoid sphenoid sinus squamous cell carcinoma with Gar-cin syndrome and an autopsy.