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肺母细胞瘤是一种罕见的肺原发性恶性瘤。Barnard(1952)首先以“肺胚胎瘤”报告一例。Spencer(1961)报告四例,其中包括Barnard之一例。他根据本瘤在组织起源上类似肾母细胞瘤,在组织上类似胎儿肺脏,故建议用“肺母细胞瘤”。至1977年国外至少有39例报告,国内则仅有一例。目前对本瘤的命名和组织起源仍有争论。现将所遇一例报告如下,并结合文献进行讨论。
Pulmonary blastoma is a rare primary pulmonary malignancy. Barnard (1952) first reported an example of “pulmonary embryonal tumor.” Spencer (1961) reported four cases, including one case of Barnard. According to his tumor, the tumor resembles nephroblastoma in histological origin and resembles fetal lung in his tissue. Therefore, it is recommended to use “pulmonary blastoma.” At least 39 cases were reported abroad by 1977 and only one case was reported in China. There is still controversy over the nomenclature and the origin of this tumor. Cases reported below are as follows and discussed in conjunction with the literature.