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克汀病患者有听力障碍临床上早已发现,其发生原因及机制至今尚未明确。作者对地方性克汀病76例及散发性克汀病11例做了一般检查,前者发生听力障碍72例(95%),后者仅1例。作者并对地方性克汀病中29例进行了较详细的检查。29例全部有语言障碍,听力正常者仅2例,余均有不同程度的听力障碍。前庭功能检查反应正常者9例,无反应者8例,反应低下者12例,其中10例有特殊的表现:计4例表现为眼震频率忽快忽慢,呈水平性及旋转性交错出现;3例表现为恐惧并有泪腺唾液腺分泌增加
Cretinism patients with hearing disorders have long been found clinically, its causes and mechanisms have not yet been defined. The authors examined 76 cases of localized cretinism and 11 cases of sporadic cretinism, with 72 (95%) hearing-impaired patients in the former and only 1 in the latter. The authors also conducted a more detailed examination of 29 cases of endemic cretinism. All 29 cases had speech impairment, only 2 cases had normal hearing, and all had hearing impairment in varying degrees. In 9 cases with normal response to vestibular function test, 8 cases had no response and 12 cases had low reaction. Among them, 10 cases had special manifestation: 4 cases manifested as sudden and slow nystagmus frequency, horizontal and rotational interlacing ; 3 cases showed fear and lacrimal gland salivary gland secretion increased