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Bertter综合征又名肾球旁器增生症,是一种继发性醛固酮增多症,1962年Bartter首次报道,国内1979年来共报道成人6例,儿童3例,现将我院所见一例报道如下:患儿,男,5岁半,因生长发育迟缓,多饮多尿5年,于1988年7月收住院。为足月平产,第4胎,母乳喂养至4个月改用米糊喂养,辅以少量牛乳,进食量极少,未服过鱼肉、蔬菜等辅食。父母非近亲婚配,家族中无类似病史。于生后4个月发病,开始出现多饮,每日饮水1000ml至1500ml,多尿,每日尿量1200ml。间常不明原因发热,肌软,不长高,智力低下,嗜睡。曾多次到外院就诊,诊断为
Bertter syndrome, also known as renal glomerular hyperplasia, is a secondary aldosteronism, Bartter for the first time in 1962 reported that in 1979 a total of 6 adult cases reported in adults and 3 children, the hospital now see an example of the report as follows : Children, male, 5 years and a half, due to growth retardation, polydipsia and polyuria for 5 years, in July 1988 admitted to hospital. For full-term pregnancy, the first 4, breastfeeding to 4 months instead of using rice paste, supplemented with a small amount of milk, eating very little, not served fish, vegetables and other food supplement. Parents are married to non-relatives and have no similar medical history in the family. 4 months after birth onset, began to drink more, daily drinking water 1000ml to 1500ml, polyuria, daily urine output 1200ml. Often unexplained fever, muscular, not tall, mental retardation, lethargy. Have repeatedly to the outside hospital for treatment, diagnosed as