2006年7月,我院收治1例在临床上隐匿性起病,主要症状为显著腹胀,主要体征为大量腹水,腹水外观呈少见的乳白色,外院CT诊断为“肝硬化、腹水”的特殊病例。但最终确诊为一种极易引起误诊的罕见病,其对腹水的临床鉴别诊断具有重要参考价值。一、初诊情况李某,男,27岁,江苏江宁人。 July 2006, admitted to our hospital in 1 cases clinically occult onset, the main symptoms of significant abdominal distension, the main signs of a large number of ascites, ascites appearance of rare milky white, outside the hospital CT diagnosis of “cirrhosis, ascites,” the special case . However, the final diagnosis is a rare and easily cause misdiagnosis of the disease, ascites clinical differential diagnosis has important reference value. First, the initial diagnosis of Lee, male, 27 years old, Jiangning, Jiangsu.