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Wilsons 病被描述为一种进行性脑退变伴肝硬化和角膜 Kayser-Fleischer 环。青少年患者肝病象征往往先于神经系症状,而且并发急性溶血性贫血。Wilson 病的肝脏表现变化很大,有描述似急性肝炎、慢性肝炎及暴发性肝炎。鉴别 Wilson 病与慢性活动性肝炎很重要,因为两者的特效疗法不同。本文报告1例急性 Wilson 病的诊治。女性18岁,既往健康。入院前3周疲乏、虚弱、腹痛、腹泻、发热,黄疸2天。以急性肝炎合并急性肝衰竭由外院转入。检查:皮肤黄染,体温38℃,角膜有 Kayser-Fleischer 环。腹部胀满,轻度积水,肝
Wilsons disease is described as a progressive brain degeneration with cirrhosis and corneal Kayser-Fleischer rings. Signs of liver disease in young patients often precede neurological symptoms, and complicated by acute hemolytic anemia. Wilson’s disease varies greatly in liver performance and has been described as acute hepatitis, chronic hepatitis and fulminant hepatitis. Identifying Wilson’s disease and chronic active hepatitis is important because of the different effects of the two. This article reports 1 case of acute Wilson disease diagnosis and treatment. Female 18 years old, past healthy. 3 weeks before admission fatigue, weakness, abdominal pain, diarrhea, fever, jaundice 2 days. Acute hepatitis with acute liver failure transferred from the outer court. Check: yellow skin, body temperature 38 ℃, cornea with Kayser-Fleischer ring. Abdominal fullness, mild water, liver