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Peutz-Jephers综合征封四之图13所附之病例有典型的色素分布,图14之病例有典型的家族史 Peutz-Jephers综合征,又称皮肤粘膜黑色素斑-胃肠道多发性急肉综合征,简称“黑斑息肉综合征”。本病的主要特征有三:①皮肤粘膜的异常色素斑点沉着。这是临床诊断的重要线索及根据。常见于口唇及颊粘膜,而以下唇为最多,其次为手指掌面及足趾跖面,其他部位少见。此种色斑有时需与雀斑、着色性干皮病、阿狄森病、砷剂或其他金属引起的黑斑病相鉴别。②胃肠道多
Peutz-Jephers Syndrome Four of Fig. 14 has attached typical cases of pigment distribution, and the case of Fig. 14 has a typical family history of Peutz-Jephers syndrome, also known as mucocutaneous melanotic plaques - multiple gastrointestinal gastrointestinal syndromes , referred to as “black spot polyposis syndrome.” The main features of the disease are three: 1 abnormal macular pigmentation of skin and mucous membranes. This is an important clue and basis for clinical diagnosis. Common in the lips and buccal mucosa, and the following lip is the most, followed by the palm of the finger and toe face, other parts are rare. Such stains sometimes need to be differentiated from freckles, xeroderma pigmentosum, Addison’s disease, arsenic, or other metal-induced melasma. 2 more gastrointestinal tract