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特发性CD4+T淋巴细胞减少症(idiopathic CD4~+T lymphocytopenia,ICL)为一种罕见的免疫缺陷病,通常在机会性感染后被发现,主要表现为机会菌感染、反复CD4~+T细胞减少,类似获得性免疫缺陷综合征(AIDS)。诊断以CD4~+T细胞减少为主要条件,但无人类免疫缺陷病毒(HIV)感染,预后较为良好。对ICL患者主要是治疗各种机会感染
Idiopathic CD4 ~ + T lymphocytopenia (ICL) is a rare immunodeficiency disease, which is usually found after opportunistic infections. It mainly manifests as opportunistic bacterial infection. Repeated CD4 ~ + T Cells are reduced, similar to Acquired Immune Deficiency Syndrome (AIDS). The diagnosis of CD4 ~ + T cell reduction as the main condition, but no human immunodeficiency virus (HIV) infection, the prognosis is good. ICL patients are mainly treated for various opportunistic infections