婴儿黑色素神经外胚层瘤(简称MNTI,下同。Melanotic neurectodermal tumourof infancy)具有不良的临床和X线表现,但其生物学行为却是良性过程的一种自相矛盾的肿瘤。自Krompecher(1918)首先报告以来,至1983年,国外文献已报道159例,国内近年来亦有零星报告随着病例报告不断增多,出现了一些恶病病例的报告,因此MNTI引起愈来愈多学者的兴趣和重视。本文报告2例,并作文献复习。病例介绍病例1,男,7个月。发现左上前牙龈肿胀4月。近来生长迅速,影响吮吸。患儿体健营养好。(?)已萌出,(?)松动Ⅱ°,上唇抬高,(?)区唇腭侧隆起的肿块约2.5×2×2cm大小,界不清,固 Infantile melanotic neuroectodermal tumors (MNTI, hereinafter referred to as Melanotic neurectodermal tumour of infancy) have poor clinical and X-ray findings, but their biological behavior is a paradoxical tumor of the benign process. Since Krompecher’s (1918) first report, by 1983, 159 cases have been reported in foreign literature. There have been sporadic reports in recent years in China. As the number of case reports has increased, there have been reports of some cases of cachexia. As a result, MNTI has become more and more frequent. Scholars’ interest and attention. This article reports 2 cases and reviews the literature. Case Introduction Case 1, male, 7 months. The upper left anterior gum was found to have swollen in April. Recently, it has grown rapidly, affecting sucking. Children have good health and nutrition. (?) Has been erupted, (?) looses the second degree, the upper lip is elevated, and the swelling of the lip and palate side of the (?) area is about 2.5 x 2 x 2 cm, and the boundary is unclear.