传统意义上的囊性肾瘤包括两种肿瘤,一种是成人型囊性肾瘤,属于混合性上皮间质肿瘤(MEST)谱系的一部分;另一种是儿童型囊性肾瘤,与DICER1基因突变相关。目前,尚无有关该肿瘤两种病变在形态学、免疫表型和基因遗传学方面详细的对比性分析。作者对比性分析12例成人型囊性肾瘤/MEST(均为女性患者,中位年龄50.5岁)和7例儿童 Traditionally, cystic nephroma includes two types of tumors, one is adult cystic nephroma and is part of the mixed epithelial mesenchymous (MEST) lineage; the other is cystic renal cell carcinoma of the child, which is associated with DICER1 Gene mutation related. At present, there is no detailed comparative analysis of morphological, immunophenotypic and genetics of the two lesions of the tumor. The authors compared 12 adult cystic nephroma / MEST (both female patients, median age 50.5 years) and 7 children