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幕上原始神经外胚叶肿瘤(sPNET)是一种较为罕见的高度恶性神经系统肿瘤,来源于原始神经上皮细胞,具有多向分化潜能,约占整个脑肿瘤的0.1%,多见于儿童,呈侵袭性生长、易播散和复发、预后很差。现回顾性分析我院2008年1月-2014年1月收治的5例儿童sPNET临床资料,总结其临床表现、影像学特征,并结合文献探讨其病理学诊断、治疗及预后。资料与方法1.一般资料5例患儿包括1例复发,男2例,
The supratentorial primitive neuroectodermal tumor (sPNET) is a rare, highly malignant tumor of the nervous system derived from primitive neuroepithelial cells with a multi-directional potential for differentiation, accounting for about 0.1% of the total brain tumor, more common in children Invasive growth, easy to disseminate and relapse, the prognosis is poor. We retrospectively analyzed the clinical data of 5 cases of children sPNET admitted in our hospital from January 2008 to January 2014, and summarized the clinical manifestations and imaging features. The pathological diagnosis, treatment and prognosis were reviewed in combination with the literature. Materials and Methods 1. General Information 5 cases of children, including 1 case of relapse, 2 males,