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婴儿期颅内肿瘤的发病率较低,婴儿家族性颅内肿瘤文献报道不多。本组2例小脑肿瘤患儿为同胞姐妹,其发病年龄、临床表现、肿瘤部位和形态特点均相似,报道如下。 例1:女性,8个月。因呕吐2月余,加剧1周,嗜睡1天于1992年2月21日入院。起表现为“溢奶”,1～2次/d,近1周呈喷射状呕吐,3～4次/d,1天前出现嗜睡.3个月时患“肺炎”。父亲2年前曾患“急性肝炎”,在化工厂工作已有7年。否认家族性肿瘤病史。入院体检:营养发育中等,神志清,反应迟钝,角弓反张位(+),前囟2.5cm×2.5cm,紧张隆起,双眼向内斜视不能外展,左鼻唇沟浅,伸舌左偏,双瞳等大、等圆,对光反射灵敏,颈项抵抗,双侧巴彬基斯征可疑阳性,四肢肌力、肌张力正常,腱反射存在。浅表淋巴结未及肿大,舟状腹。实验室检查:三大常规正常范围,血沉3mm/
The incidence of intracranial tumors in infancy is low, few reports of familial intracranial tumors in infants. The group of 2 cases of cerebellar tumor children siblings, their age of onset, clinical manifestations, tumor site and morphological characteristics are similar, are reported below. Example 1: Female, 8 months. Due to vomiting more than 2 months, an increase of 1 week, lethargy 1 day in February 21, 1992 admission. From the performance of “overflowing milk”, 1 or 2 times / d, nearly 1 week was jet-like vomiting, 3 to 4 times / d, 1 day before drowsiness .3 months suffering from “pneumonia.” My father had “acute hepatitis” 2 years ago and has worked in a chemical plant for 7 years. Denied the history of familial tumors. Admission examination: nutritionally developed, conscious, unresponsive, angle arch reverse (+), anterior fontanel 2.5cm × 2.5cm, tension uplift, esotropia can not be outreach, left nasolabial fold shallow, left tongue extension , Double pupil and other large, round, sensitive to light reflex, neck resistance, bilateral Papan Keith sign doubtful positive, muscle strength, muscle tone, tendon reflex exists. Superficial lymph nodes less than enlargement, scaphoid. Laboratory tests: the three normal range, ESR 3mm /