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真两性畸形颇为少见,我们近年收治2例,报告如下: 例一、刘某、社会性别女性,22岁,因外生殖器异常,乳房发育差前来就诊,患者出生时就发现外生殖器异常,从未来过月经,无周期性血尿。查体:女性装扮,喉结略隆起,肩宽骨盆窄,乳房发育差,阴毛女性分布,阴蒂明显增大如5岁儿童阴茎大小,有包皮可向后翻转,龟头尖端有一小孔,为仅0.3厘米深之盲端。阴道部位有一圆形小口,可导出清亮尿液。阴道深约5厘米,未发现宫颈,肛门指诊盆腔空虚。实验室资料:尿17-羟21.7mg/24h,尿17-酮20.9mg/24h,性染色体核型检查为46XX。行剖腹探查术,术
True hermaphroditism is quite rare, we have treated 2 cases in recent years, the report is as follows: Case 1, Liu, gender female, 22 years old, due to genital abnormalities, breast development to come to the clinic, the patient was found to be genital abnormalities at birth, Menstruation from the future, no periodic hematuria. Physical examination: female dress up, slightly enlarged laryngeal, narrow pelvis of shoulder, poor breast development, pubic hair distribution, clitoris significantly increased, such as 5-year-old children with penile size, foreskin can flip back, tip of the glans has a small hole, only 0.3 Centimeter deep blind end. Vaginal part of a circular small mouth, can lead to clear urine. Vaginal depth of about 5 cm, did not find the cervix, anus, pelvic emptiness. Laboratory data: urine 17-hydroxy 21.7mg / 24h, urinary 17-ketone 20.9mg / 24h, sex chromosome karyotype examination for 46XX. Laparotomy exploration, surgery