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报告20例Sturge-Weber综合征,并根据临床资料分析讨论如下。 临床资料 男女各10例。年龄10~46岁。1例其母和妹枕部有血管痣。2例其母在妊娠早期有外伤史。 症状和体征 1.皮肤血管痣:20例均有面部血管痣。颜色由粉红到紫色。分布于全面部者4例;三叉神经第I、Ⅱ支者14例;第Ⅲ支者8例,累及颈、胸、躯干及四肢者7例。其中3例患侧下肢较健侧肥大,深层伴有海绵状血管瘤和皮肤静脉曲张。1例右
Report 20 cases of Sturge-Weber syndrome, and based on clinical data analysis is discussed below. Clinical data of 10 men and women. Age 10 to 46 years old. 1 case of the mother and sister occipital vascular nevus. 2 cases of her mother had a history of trauma in early pregnancy. Symptoms and signs 1. Vascular nevus: 20 cases have facial nevus. Color from pink to purple. Four cases were found in the entire department. There were 14 cases with branches I and II of trigeminal nerve and 8 cases with branches III and 7 cases with neck, chest, trunk and limbs. 3 cases of ipsilateral lower limbs than the contralateral hypertrophy, deep cavernous hemangiomas and skin varicose veins. 1 case right