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组织细胞增多症是由单核巨噬细胞系细胞增生所致,可发生于任何年龄组,分为良性和恶性型,或组织细胞增多症X和非-X组织细胞增多症两大类。组织细胞增多症X(HX) HX病因未明,其特点为一种特殊型的组织细胞(胞浆内含有郎格罕颗粒,LG)增生。包括三种临床类型:Letterer—Siwe病(LSD),Hand—Sehuller—Christian(HSC)病和嗜酸性肉芽肿(EG)。当累及两个以上组织或器官时称为播散性HX。临床类型: LSD:1/3病例于生后6个月内起病,其余大部分病例于2岁前发病。约半数患者起病时即有皮损,预后恶劣。典型皮损为直径
Histiocytosis is caused by the proliferation of mononuclear macrophage cell lines and can occur in any age group and is divided into two groups, benign and malignant, or histiocytosis X and non-X histiocytosis. X-ray histiocytosis X (HX) HX etiology is unclear, characterized by a special type of tissue cells (the cytoplasm containing Langerhans particles, LG) hyperplasia. There are three clinical types: Letterer-Siwe disease (LSD), Hand-Sehuller-Christian (HSC) disease and eosinophilic granuloma (EG). Disseminated HX is called when more than two tissues or organs are involved. Clinical types: LSD: 1/3 of the cases started within 6 months after birth, and most of the remaining cases occurred before the age of 2. About half of patients have skin lesions at the time of onset and have a poor prognosis. Typical skin lesions are diameters