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报告一不平常的颞骨多发性骨髓瘤伴有眩晕、耳鸣、耳聋及舌下神经瘫痪的病例,既往文献未见报告过。多发性骨髓瘤典型者为单系丙种球蛋白病(monoelonic gammopathy),本文报告者为双系丙种球蛋白病(biclonic gammopathy),极少见,为非典型性(Nussbaum,1973)。本文病例为55岁白种妇女,患耳聋、眩晕及右耳周痛而入院。患者过去身体健康,1975年发生间歇性右耳痛而被当作慢性乳突炎进行治疗,1976年出现右耳鸣与缓慢进行性聋伴有右额颞部头钝痛,6周前眩晕,3周前显现右舌下神经瘫痪。入院查见右乳突尖及胸锁乳突肌上端呈现轻度肿胀和压痛,无眼震,舌瘫痪,伸出时偏右。血象正常,血沉52 mm/小时,血细胞比容34.1%,尿酸7.0,钙10.8,磷4.9,血清总蛋白10.6克%,白蛋白3.6克%。尿蛋白微量和Bence Jones蛋
Report an unusual temporal bone multiple myeloma with dizziness, tinnitus, deafness and sublingual nerve paralysis cases, no previous literature has been reported. A typical case of multiple myeloma is monoelonic gammopathy, a report of biclonic gammopathy, rare and atypical (Nussbaum, 1973). This case is a 55-year-old white woman hospitalized with deafness, dizziness and right ear pain. Patients in the past in good health, intermittent right ear pain in 1975 and was treated as chronic mastoiditis, right tinnitus in 1976 and slow progressive deafness accompanied by right frontotemporal dull pain, vertigo 6 weeks ago, 3 A week ago showed the right hypoglossal nerve paralysis. Admitted to see the right mastoid tip and sternocleidomastoid muscle showed mild swelling and tenderness, no nystagmus, paralysis of the tongue, when extended to the right. Normal blood, erythrocyte sedimentation rate 52 mm / h, hematocrit 34.1%, uric acid 7.0, calcium 10.8, phosphorus 4.9, serum total protein 10.6 g%, albumin 3.6 g%. Urinary protein trace and Bence Jones egg