患者女,60岁,出生时左耳垂及腮部即有一半球形、约鸡蛋大小肿块,后逐渐增大,至23岁时肿块底部平下颏。近10年肿块生长迅速,就诊时底部平左大腿中部。体检见自左耳垂、左颈肩部起有一囊袋状肿块向下悬垂,底部平左大腿中下1/3交界处,大小为80×25×10cm,质软,表面见咖啡色斑。躯干及四肢有百余个散在结节样肿物,约黄豆大,突出皮肤表面 The female patient, 60 years old, was born with a hemisphere of left earlobe and ankle, which was half spherical and about the size of an egg, and then gradually enlarged until the age of 23 when the tumor was flat at the bottom. In the past 10 years, the masses grew rapidly. At the time of treatment, the bottom was flat and the middle of the left thigh was flat. Physical examination revealed a pocket-like mass from the left ear lobe, left neck and shoulder, and a downward drape. The bottom of the left lower thigh was flat and the lower third of the junction was 80×25×10 cm in size. It was soft and covered with coffee spots on the surface. There are more than 100 scattered nodular masses on the trunk and limbs, about soy beans, prominent skin surface