遗传性球形红细胞增多症(HS)是一种遗传性溶血性贫血,以不同程度贫血、间发性黄疸、脾肿大、球形红细胞增多及红细胞渗透脆性增加为特征。若患有HS的妇女处于妊娠状态,对母体及胎儿都有巨大影响。目前,HS并发脾肿大、溶血危象且合并足月妊娠的病例在国内外文献中并无报道,我院近期收治1例此类患者。现报道如下。 Hereditary spherocytosis (HS) is a hereditary hemolytic anemia characterized by varying degrees of anemia, idiopathic jaundice, splenomegaly, spherocytosis, and increased red cell osmotic fragility. If the woman with HS in pregnancy, both maternal and fetal have a tremendous impact. Currently, HS complicated by splenomegaly, hemolysis crisis and cases of full-term pregnancy merger in the literature has not been reported in our hospital, our hospital recently admitted to such a patient. Report as follows now.