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色素性绒毛结节性滑膜炎(pigmented villondular synov itis,PVNS)是罕见的滑膜瘤样增生性病变,其特点是滑膜弥漫增生,大体上形成大量绒毛,镜下有大量含铁血黄素沉着。由于对该病的认识不足,患者常被误诊误治。本院及吉林省肿瘤医院共诊治4例,结合典型病例并复习文献,探讨临床、影像学、病理特征及治疗、预后,以提高对本病的认识。1临床资料本组共4例,男2例,女2例,年龄38~54岁,平均年龄45岁。发生部位在膝关节2例,踝关节1例,足关节1例,病程6个月~2年,术后复发1例。临床表现:受累关节不
Pigmented villondular synovitis (pigmented villondular synovitis, PVNS) is a rare synovial tumor-like proliferative disease characterized by diffuse synovial proliferation, the formation of a large number of villi in general, a large number of hemosiderin calm. Due to lack of understanding of the disease, patients are often misdiagnosed and mistreated. The hospital and Jilin Provincial Tumor Hospital in 4 cases were diagnosed and treated, combined with typical cases and review the literature to explore clinical, imaging, pathological features and treatment, prognosis, in order to improve awareness of the disease. A clinical data of this group a total of 4 cases, 2 males and 2 females, aged 38 to 54 years, mean age 45 years. Occurred in the knee in 2 cases, ankle in 1 case, foot joint in 1 case, duration of 6 months to 2 years, 1 case of recurrence. Clinical manifestations: affected joints are not