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间叶性软骨肉瘤较少见,其原发瘤及多器官转移瘤术后能长期存活者很罕见。国内报道50余例,皆无长期存活,我科收治1例原发于肋骨后发生肺及甲状腺转移,经多次手术已存活25年。男,42岁。1966年4月在外院切除右第6肋骨肿瘤,病理诊断为间叶性软骨肉瘤。1983年3月以左侧甲状腺肿物3×2×2cm及胸片示右上肺5×3.5cm圆形致密阴影,临床诊断为甲状腺癌肺转移而入院。先行左叶甲状腺次全切除,2个月后行右肺上叶切除。病理诊断甲状腺及肺间叶性软骨肉瘤(转移性)。
In rare cases, indifferent chondrosarcomas of the lobar chondrosarcoma are rare in patients with primary tumors and multi-organ metastases who have long-term survival after surgery. More than 50 cases were reported in China, and there was no long-term survival. In our department, one case of primary lung and thyroid metastasis occurred after the ribs and survived for 25 years after multiple operations. Male, 42 years old. In April 1966, the right sixth rib tumor was excised in the outer court. The pathological diagnosis was mesenchymal chondrosarcoma. In March 1983, the left thyroid mass was 3 × 2 × 2 cm and the chest X-ray showed a dense shadow of 5 × 3.5 cm in the upper right lung. The patient was admitted to the hospital with a clinical diagnosis of lung metastases from thyroid cancer. The left lobe was first removed and the right upper lobe was removed 2 months later. Pathological diagnosis of thyroid and pulmonary interchondral chondrosarcoma (metastatic).