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本文报告10例小儿克山病心肌病变的电镜观察结果。看到受累的细胞器主要是心肌线粒体、外膜系统和肌原纤维等。其中以线粒体的形态改变最为突出。线粒体的主要变化是肿胀、基质清亮、嵴严重破坏、基质电子致密物质沉着和线粒体数量增多等。线粒体改变具有广泛性、严重性和早发性的特点。还描述了两种形态改变的线粒体。认为心肌线粒体的改变在克山病发病机制中可能具有原发性意义。
This article reports 10 cases of pediatric Keshan disease myocardial lesions observed by electron microscopy. To see the main organelles involved in myocardial mitochondria, adventitial system and myofibrils. Among them, the change of mitochondrial morphology is the most prominent. The main changes in mitochondria are swelling, clear substrate, crest severely damaged, dense matrix electron dense material and the increase in the number of mitochondria. Mitochondrial changes have the characteristics of extensive, serious and early onset. Two morphologically altered mitochondria are also described. It is thought that the alteration of myocardial mitochondria may have the primary significance in the pathogenesis of Keshan disease.