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目的:提高对TAFRO综合征的认识。方法:报道1例TAFRO综合征的临床特征、实验室检查指标、诊治经过及转归,并进行相关文献复习和讨论。结果:女,68岁,因头晕乏力20余年,加重伴胸闷气喘20余天入院。患者有发热、脾脏肿大、双下肢水肿、多浆膜腔积液贫血、血小板减少;骨髓活检病理显示间质网状纤维组织增生显著,淋巴浆细胞聚集。经糖皮质激素及静脉用丙种球蛋白免疫调节治疗、输注红细胞、血小板支持治疗后,患者体温恢复正常、浆膜腔积液吸收、血象恢复良好。结论:TAFRO综合征是一组临床症状的组合,准确诊断有赖于综合临床表现、实验室检查及病理学特征,糖皮质激素治疗为首选治疗,配合积极支持治疗,预后显著改善,临床上需提高对该疾病的认识。
Objective: To improve the understanding of TAFRO syndrome. Methods: One case of TAFRO syndrome was reported, including clinical features, laboratory tests, diagnosis and treatment, and prognosis. Relevant literatures were reviewed and discussed. Results: Female, 68 years old, due to dizziness, fatigue more than 20 years, increased with chest tightness and asthma more than 20 days admitted. Patients had fever, splenomegaly, edema of both lower extremities, anemia of pleural effusion, thrombocytopenia; bone marrow biopsy showed interstitial reticular fibrous tissue hyperplasia, lymphocyte aggregation. Glucocorticoid and intravenous immunoglobulin immunomodulatory therapy, transfusion of red blood cells, platelet support treatment, the patient returned to normal temperature, serous fluid absorption, blood recovery was good. Conclusion: TAFRO syndrome is a combination of clinical symptoms, accurate diagnosis depends on the clinical manifestations, laboratory tests and pathological features, glucocorticoid therapy is the preferred treatment, with active supportive care, the prognosis was significantly improved, the clinical need to be improved Awareness of the disease.