肝外发育型肝癌系指肝内癌肿病变不明显,而癌瘤主要向肝外生长增殖的肝癌,较为罕见。1891年Cristiani 首次报告本病。作者回顾1985～1990关西医科大学外科诊治的26例并复习文献报告的99例(1891～1989年)肝外发育型肝癌,就其分类、临床特征、诊断及治疗方法进行了探讨。综合本组26例及文献报告99例资料,肝外发育型肝癌发病年龄高峰为50～60岁。男性为多(男:女=87∶35)。源于肝右叶者62例;左叶55例;尾叶10例;肝外异位者3例。癌瘤直径均在5～10 cm 以 Extrahepatic developmental hepatocellular carcinoma refers to the intrahepatic cancer lesions are not obvious, and the cancer is mainly to extrahepatic growth and proliferation of liver cancer, is relatively rare. In 1891 Cristiani first reported the disease. The author reviewed 26 cases of surgical treatment at the Kansai Medical University from 1985 to 1990 and reviewed 99 cases (1891 to 1989) of extrahepatic developmental liver cancer reported in the literature. The classification, clinical features, diagnosis, and treatment methods were discussed. Comprehensive group of 26 cases and 99 cases of literature reports, extrahepatic developmental liver cancer peak age of 50 to 60 years old. There are many men (male: female = 87:35). From the right lobe in 62 cases; the left lobe in 55 cases; 10 cases of the tail; extrahepatic ectopic in 3 cases. The tumors are 5 to 10 cm in diameter