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10年中著者遇硬结症100例,说明此病并不少见,分析如下:年龄:小于20岁6例、21—30岁48例、31—40岁28例、40—50岁8例、超过51岁10例。症状:鼻堵94例、鼻畸形32例、声哑16例、上唇肿胀10例、喉部不适6例及泪溢4例。病变部位:鼻部94例、腭部22例、咽部8例、喉部16例、上唇10例、泪囊4例及眼眶1例。就诊时病程不同,早期表现为皮肤增厚变硬;晚期病变部被摧毁。硬结症常开始于鼻中隔粘膜下或鼻翼,逐渐扩展至鼻咽、喉、支气管、唇、舌、悬雍垂、软腭及眼眶等。病变如已侵犯骨部,可产生可怕的外貌及畸形。Kakar等(1968)报告一例鼻硬结症拟似上颌骨恶性肿物。Badrawy
10 years, the authors encountered sclerosis in 100 cases, indicating that the disease is not uncommon, the analysis is as follows: Age: less than 20 years in 6 cases, 21-30 years in 48 cases, 31-40 years in 28 cases, 40-50 years old in 8 cases, more than 51 years old in 10 cases. Symptoms: nasal blocking in 94 cases, nasal deformity in 32 cases, dumbness in 16 cases, upper lip swelling in 10 cases, 6 cases of laryngeal discomfort and 4 cases of tearing. Lesions: nose 94 cases, 22 cases of palate, pharyngeal in 8 cases, 16 cases of throat, upper lip in 10 cases, 4 cases of lacrimal sac and 1 case of orbital. Different duration of treatment, the early manifestations of thickening of the skin thickening; advanced lesion was destroyed. Sclerosis often begins in the nasal septum or nose, gradually extended to the nasopharynx, larynx, bronchus, lips, tongue, uvula, soft palate and orbital and so on. If the lesion has been violated bone, can have terrible appearance and deformity. Kakar et al. (1968) reported a case of rhinosclerosis similar to maxillary malignancies. Badrawy