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原发性下腔静脉肿瘤(Primary Tumor of IVC∶PTIVC)从 Perl 在1871年首例报道至1954年,文献记载仅8例,列为罕见。此后,报道病例增多,止1985年,共累计93例,证明近期发病率在增加。在这93例中,绝大多数(95.7%)是下腔静脉平滑肌肉瘤(表1),是一个棘手的治疗问题。随着近代诊斯方法的问世和血管外科的发展,使 PTIVC 的早期诊断及根治性切除成为可能。本文就其病因、病理、临床表现、预后及其外科治疗方面的进展作一综述。
Primary Tumor of IVC (PTIVC) was reported from the first case of Perl in 1871 to 1954. Only 8 cases were reported in the literature and it is rare. Since then, the number of reported cases has increased, and in 1985, a total of 93 cases have been accumulated, which proves that the recent incidence is increasing. In these 93 cases, the vast majority (95.7%) of the inferior vena cava leiomyosarcoma (Table 1) was a thorny treatment problem. With the advent of modern diagnostic methods and the development of vascular surgery, early diagnosis and radical resection of PTIVC have become possible. This article reviews the etiology, pathology, clinical manifestations, prognosis, and progress of surgical treatment.