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常见变异型免疫缺陷病(Common rariableim munodeficiency)是一种最常见的全低丙种球蛋白血症。现将住院患儿筛选出的4例报告如下。病例摘要例1:男,13岁。反复咳喘12年,出生6个月后多次患肺炎,先后住院30余次。鼻搧及三凹征(+),咽后壁淋巴滤泡增生,扁桃体Ⅰ°肿大,双肺闻及中等量小水泡音,肝剑突3cm,肋下2.5cm,脾肋下4.5m。X线示双肺中、内带散在片状阴影,实验室检查见表。诊断为:①支气管肺炎。②低丙种球蛋白血症。经多次输血浆、肌注丙种球蛋白后,痊愈出院。例2:男,10岁。自4岁时患百日咳后经常咳嗽,
Common variant immunodeficiency disease (Common rariableim munodeficiency) is one of the most common low gammlasia. Now inpatient screening of 4 cases reported as follows. Case Summary Example 1: Male, 13 years old. Cough repeatedly 12 years, six months after birth suffering from pneumonia, has more than 30 inpatients. Nasal fan and the three concave sign (+), pharyngeal lymphoid follicular hyperplasia, tonsil I ° enlargement, lung smear and a small amount of moderate sound, liver xiphoid 3cm, ribs 2.5cm, spleen ribs 4.5m. X-ray showed lungs, flaky shadows within the strip, laboratory tests see the table. Diagnosed as: ① bronchial pneumonia. ② low gammaglobulinemia. After repeated blood transfusion, intramuscular gamma globulin, cured and discharged. Example 2: Male, 10 years old. Since the age of 4, after suffering from whooping cough often cough,