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本文通过分析出血型烟雾病的临床特点,探讨其治疗方法。报告经CT扫描确诊的出血型烟雾病18例,男5例,女13例,年龄11岁~75岁,平均41.2岁。第一次出血者16例(未包括CT扫描普及前出血的2例),其中基底节出血7例(43.8%),不伴有明显脑内出血的一次性脑室内出血6例(37.5%),丘脑出血(同时均伴有脑室内出血)2例(12.5%),脑皮质下出血1例(6.3%)。一次性和二次性脑室内出血病例共计可达50%的高发率。一次性脑室内出血者一般预后良好,而脑实质内出血者因其出血部位和出血量的不同,预后也不一样。发生第一次出血者平均观察4.4年,其预后:中残以上的预后良好者占72.2%,死亡率5.6%。发生再出血者5例(占27.8%),平均观察4年~5年。再出血发生1次者4例,2次者1例,共计6次。第一次出血至发生再出血的时间为2周~18年,其间隔时间越
This article analyzes the clinical features of bleeding moyamoya disease, explore its treatment. Reported by CT scan of haemorrhagic moyamoya disease in 18 cases, 5 males and 13 females, aged 11 to 75 years, mean 41.2 years. The first bleedings were performed in 16 patients (2 not including pre-hemorrhage of CT scan), including 7 cases of basal ganglia hemorrhage (43.8%), 6 cases (37.5%) of single intracerebral hemorrhage without obvious intracerebral hemorrhage, Bleeding (accompanied by intraventricular hemorrhage in 2 cases) was found in 12.5% and in 1 case (6.3%) in cerebral cortex. One-time and secondary intraventricular hemorrhage cases total up to 50% of the high incidence. One-time intraventricular hemorrhage generally prognosis is good, and intraparenchymal hemorrhage because of its bleeding site and the amount of bleeding, the prognosis is not the same. The first bleeding occurred in an average of 4.4 years of observation, the prognosis: the prognosis of moderate and severe residual accounted for 72.2%, the mortality rate of 5.6%. Rebleeding in 5 cases (27.8%), the average observation of 4 years to 5 years. Bleeding occurred once in 4 cases, 2 times in 1 case, a total of 6 times. The first bleeding to rebleeding occurred in two weeks to 18 years, the more time interval