进行性系统性硬化症(progressiye Systemic Sclerosis 简称 pss)。本病临床表现复杂,多数病人随病情发展而累及内脏,但也有少数在皮肤改变之前即有内脏受累,常造成临床诊断困难。本文将我院1978～1984年收治的30例分析报道如下。 Progressive Systemic Sclerosis (pSS). The clinical manifestations of this disease is complex, most patients with the development of disease involving the internal organs, but there are a few in the skin before the change that visceral involvement, often resulting in clinical diagnosis difficult. This article will be our hospital from 1978 to 1984 admitted 30 cases reported as follows.