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作者连续遇到3例晚期Duchenne’s肌营养不良症(DMD),均有扩张性心肌病(dilated cardiomyopathy),内2例发生肺血栓栓塞.例1,男,8岁诊断DMD.16岁患过充血性心衰.6月后咳嗽、呼吸困难入院.血象高,胸片示右下肺浸润.超声心动图示心脏射血分数<10%,左室内附壁血栓;无室壁节段性异常.肺部核素扫描诊断右下肺栓塞.其凝血酶原时间延长至18.5秒.肝素治疗无效,入院第9日死亡,未尸解.例2,男,4岁诊断为DMD.17岁患过充血性心衰.11月后胸痛,咳嗽,进行性呼吸困
The authors encountered three consecutive cases of Duchenne’s Muscular Dystrophy (DMD), both with dilated cardiomyopathy, and two with pulmonary thromboembolism in Example 1. Male, 8 years old Diagnosing DMD, Cough, dyspnea admitted to hospital after 6 months, high blood count, chest X-ray showed right lower lung infiltrate, echocardiography showed cardiac ejection fraction <10%, left ventricular wall thrombosis; Department of radionuclide scan diagnosis of right lower pulmonary embolism.The prothrombin time was extended to 18.5 seconds.Hiver therapy is invalid, died on the 9th day of admission, not autopsy.Example 2, male, 4 years old diagnosed as DMD.17 years old suffering from hyperemia 11 months after chest pain, cough, sleepy breathing difficulties