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原发于大涎腺的肉瘤很罕见,约占所有涎腺肿瘤的0.3%到1.5%。本文介绍了11例原发于腮腺的肉瘤其临床病理特征。患者男性8人,女性3人,年龄7~75岁,平均42岁。11例肉瘤包括:3例恶性纤维组织细胞瘤;神经肉瘤、横纹肌肉瘤、纤维肉瘤和骨肉瘤各2例。所有患者均主诉腮腺区无痛性增大的包块,发现2周至10个月不等,3例出现面瘫,就诊时均未发现颈淋巴结转移。治疗根据临床分期(肿瘤大小)决定首次手术。
The sarcoma that originates in the parotid gland is rare, accounting for approximately 0.3% to 1.5% of all parotid gland tumors. This article describes the clinical and pathological features of 11 cases of primary sarcoma in the parotid gland. The patients were 8 males and 3 females, aged 7 to 75 years, with an average age of 42 years. 11 cases of sarcoma included: 3 cases of malignant fibrous histiocytoma; 2 cases of neurosarcoma, rhabdomyosarcoma, fibrosarcoma, and osteosarcoma. All patients complained of painlessly enlarged parotid masses, ranging from 2 weeks to 10 months, with facial paralysis in 3 cases. No lymph node metastasis was found during the visit. Treatment depends on the clinical stage (tumor size) to determine the first surgery.