烟雾病是一种罕见的颅内血管病变，通过对干燥综合征所致成人烟雾病单发病例资料及临床特征分析发现，烟雾病在儿童多为先天性血管发育异常所致，而成人则以出血表现为主。DSA能准确显示烟雾病病变血管的部位和程度，显示侧支循环途径及脑底异常血管网，目前仍被认为是诊断烟雾病的金标准。该病目前还没有十分理想的治疗方法，针对病因和症状进行治疗效果满意。康复期患者仍应继续控制血压等脑血管病的相关危险因素。“,”Moyamoya disease is a rare intracranial vascular lesions and studies of single cases data and clinical features of adult moyamoya disease due to sjogren syndrome discovered that children moyamoya diseases were caused by congenital vascular malformation (CVM ) and hemorrhage was the main manifestation of a‐dult moyamoya disease .The DSA could accurately show the sites and degrees of pathological vessels ,collateral circulation pathway and abnormal basal vascular network and was known as the gold standard of moyamoya disease diagnosis at present .T here is no ideal treatment for the disease at present and the effectiveness of treatment aimed at causes and symptoms is satisfactory .Related risk factors of cerebrovascular disease should be continuously controlled for convalescence patients .