患者女,21岁,进行性双下肢活动障碍1个月伴排尿困难,加重1周。体检见双下肢肌力Ⅳ级,双膝反射亢进,双侧Babinski征阳性。外院脊柱MRI示胸腰段椎管内多发占位病变。于外院行手术切除椎管内4个肿瘤,病理结果不确定,考虑为神经纤维瘤可能性大。9个月后患者再次出现双下肢酸痛,行走 Female, 21 years old, progressive lower extremity dysfunction 1 month with dysuria, aggravating 1 week. Physical examination showed lower limb muscle strength grade Ⅳ, knee hyperreflexia, bilateral Babinski sign positive. Spinal MRI showed thoracolumbar spinal canal multiple occupying lesions. Surgical removal of the spinal cord in the outer hospital 4 tumors, the pathological findings uncertain, consider the possibility of neurofibromas. After 9 months, the patient again had lower extremity soreness and walking