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脊椎骨骺发育不良(spondylo epiphyseal dysplasia,以下简称SD)并非少见。在S D中有喉气管发育不良者未见报导。作者评述两例。例1男性9岁,有呼吸困难和反复“哮喘”史。4年住院12次,两次气管切开。除SD的多发骨病变外,视神经发育不良,小脑和上下运动神经元功能障碍。喉镜检查,自环状软骨至第三气管环明显增厚呈环形狭窄。用肋软骨移植的喉气管成形术治疗,失败后仍用气管切开套管,继续遭受原发病变加重的痛苦。例2男性17岁,自8岁起有进行性呼吸困难,多次“哮喘”史。气管切开近一年。喉镜检查,声门上有许多粘膜皱折,声门完全闭塞。用Oo远窥镜检查,声门后方见一极小开口,声门下严重狭窄,声带增厚短缩,
Spondylo epiphyseal dysplasia (hereinafter referred to as SD) is not uncommon. There was no report of laryngotracheal dysplasia in SD. The authors review two cases. Example 1 Male 9 years old with dyspnea and repeated “asthma” history. 4 years in hospital 12 times, twice tracheotomy. In addition to multiple bone lesions of SD, optic nerve dysplasia, cerebellar and upper and lower motor neurons dysfunction. Laryngoscopy, from the annular cartilage to the third tracheal ring significantly thickening ring-shaped stenosis. Laryngeal tracheal angioplasty with costal cartilage transplantation, after the failure is still tracheotomy tube, continue to suffer from the aggravation of the primary lesion. Example 2 A 17-year-old man with progressive dyspnea and multiple “asthma” episodes since the age of 8 years. Tracheotomy nearly a year. Laryngoscopy, supraglottic mucosal folds, glottis completely occluded. With Oo far endoscopic examination, see a very small opening behind the glottis, severe subglottic stenosis, vocal cord thickening shortening,