心肌致密化不全(noncompaction of ventricular my-ocardium,NVM)是以心室内异常粗大的肌小梁和交错的深陷隐窝为病理特征的心肌病,是一种少见的先天性心脏畸形。目前WHO将其归类于不定型的心肌病。到目前为止,国外文献报道仅200余例。近几年随着对该病认识的加深和诊断技术的 Noncompaction of ventricular my-ocardium (NVM) is a cardiomyopathy characterized by abnormally large intramyocardial trabecular meshwork and staggered deep crypts and is a rare congenital heart malformation. At present, WHO classified it as unfixed cardiomyopathy. So far, only 200 cases have been reported in foreign literature. In recent years as the understanding of the disease deepen and diagnostic techniques