颅内原发性恶性淋巴瘤是指用现代诊断技术证实时病变仅局限于脑内的一种非霍奇金淋巴瘤。本病临床较少见,发病机制仍不明确,术前诊断误诊率较高,通过影像学检查,结合脑脊液细胞学检查及免疫组化分析可提高术前诊断准确率,并与颅内其他疾病相鉴别。病理检查仍是目前诊断颅内原发性恶性淋巴瘤的金标准。 Intracranial primary malignant lymphoma is the use of modern diagnostic techniques to confirm that when the lesion is confined to the brain of a non-Hodgkin’s lymphoma. The disease is relatively rare, the pathogenesis is still not clear, preoperative diagnosis of misdiagnosis rate is high, by imaging studies, combined with CSF cytology and immunohistochemistry analysis can improve the accuracy of preoperative diagnosis, and other intracranial diseases Phase identification. Pathological examination is still the gold standard for the diagnosis of intracranial primary malignant lymphoma.