先天性无虹膜是一种以明显的完全性虹膜缺损为特征并伴有多种眼部先天性异常的遗传病。我们在临床上遇到一家系 ,且有明显的遗传倾向 ,现报告如下。1　病例报告先证者Ⅰ ,患者女 ,16岁 ,自幼视物模糊不清伴羞明至来诊。 5年前曾在当地某医院行“白内障手术”(术名不详 )后视物 Congenital aniridia is a genetic disease characterized by a marked complete iris defect accompanied by a variety of congenital abnormalities in the eye. We met a clinical department, and a clear genetic predisposition, are as follows. 1 case report probands Ⅰ, the patient female, 16 years old, blurred vision since childhood with companion came to the clinic. 5 years ago in a local hospital “cataract surgery” (name unknown) rear view