无色素性视网膜色素变性为原发性视网膜色素变性的一种特殊类型,临床较少见。自1979年以来,我们共收治本病6例,现将其临床、辅助检查及治疗结果报告如下。 6例中,男性3例,女性3例。发病年龄15～27岁,平均23.6岁。均为双眼患病,视力:0.03者1例(2只眼).0.1者4例(8只眼),1.2以上者1例(2只眼)。6例均有夜盲史,均为散发病例,其中1例双眼均合并闭角型青光眼。眼底检查:视盘边界整齐(4例)或稍模糊(2例),色腊黄。视网膜色淡,略呈 Achromatic retinitis pigmentosa is a special type of primary retinitis pigmentosa, clinically rare. Since 1979, we received a total of 6 cases of this disease, now its clinical, laboratory examinations and treatment results are reported below. 6 cases, 3 males and 3 females. The onset age of 15 to 27 years, mean 23.6 years old. All eyes were affected, visual acuity: 0.03 in 1 case (2 eyes) .0.1 in 4 cases (8 eyes), 1.2 or more in 1 case (2 eyes). 6 cases had night blindness, were sporadic cases, including 1 case of both eyes with angle-closure glaucoma. Fundus examination: optic disc border neat (4 cases) or slightly blurred (2 cases), color wax yellow. Retina pale, slightly