先天性遗传性球形红细胞增多症是一种常染色体显性遗传的家族性疾病是红细胞膜缺陷导致的最常见的溶血性贫血该病极易误诊脾切除有明显疗效患儿男10 岁因面色苍白乏力9 年余加重伴巩膜黄染10 天入院患儿于出生4 个月时家长发现面色较苍白逐年加重伴乏力有时尿色黄曾在当地诊为? Congenital hereditary spherocytosis is an autosomal dominant familial disease is the most common hemolytic anemia caused by erythrocyte membrane defects misdiagnosis of the disease is extremely misdiagnosed splenectomy has a significant effect in children at age 10 due to pale face More than 9 years of aggravating sclera with yellow dye stained 10-day admission to children at 4 months of age parents found pale compared with the increasing year by year with weakness sometimes urinary yellow was diagnosed locally?