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Introduction Wilson’s disease is a rare inherited disorder of copper metabolism which is characterized by the inability to secrete the copper-ceruloplasmin complex into plasma and free copper into the bile.In the liver,the copper deposits in the periportal regions and incites an inflammatory reaction,resulting in chronic liver disease[1].Untreated Wilson′s disease is progressive and fatal,so the early diagnosis is important for working out treatment strategy[2].However,the majority of liver imaging findings do not show characteristic change that leads to the difficulty of differential diagnosis.US,CT and magnetic resonance imaging (MRI) findings of liver can reveal the non-specific hepatic injury including increased echogenicity of the liver,irregularity of contours and atrophied right liver lobe.This article presents a case of Wilson’s disease and provides a detailed review of relevant literature.
Introduction Wilson’s disease is a rare inherited disorder of copper metabolism which is characterized by the inability to secrete the copper-ceruloplasmin complex into plasma and free copper into the bile. The liver, the copper deposits in the periportal regions and incites an inflammatory reaction, resulting in chronic liver disease [1] .Untreated Wilson’s disease is progressive and fatal, so the early diagnosis is important for working out treatment strategy [2] .However, the majority of liver imaging findings do not show characteristic change that leads to the difficulty of differential diagnosis .US, CT and magnetic resonance imaging (MRI) findings of liver can reveal the non-specific hepatic injury including increased echogenicity of the liver, irregularity of contours and atrophied right liver lobe. this article presents a case of Wilson’s disease and provides a detailed review of relevant literature.