平山病又称青年上肢远端肌萎缩症,是日本学者平山惠造在1959年首先报道的一种良性自限性运动神经元疾病。与运动神经元病中的肌萎缩侧索硬化、进行性脊肌萎缩和多灶性运动神经病等相似,易混淆,临床诊断本病时需加以鉴别。资料与方法平山病诊断依据1.临床依据:①青年早期隐袭起病,男性多见;②局限于上肢远端,手指及腕无力,伴手和前臂远端肌 Pingshan disease, also known as the young upper limb distal muscular atrophy, is the Japanese scholar Hirayama made in 1959 first reported a benign self-limiting motor neuron disease. And motor neuron disease in amyotrophic lateral sclerosis, progressive spinal muscle atrophy and multifocal motor neuropathy and other similar, easily confused, the clinical diagnosis of the disease to be identified. Materials and Methods Pingshan disease diagnosis based on 1. Clinical basis: ① youth early insidious onset, more common in men; ② limited to the distal upper limbs, fingers and wrists, accompanied by forearm and distal muscles