血友病是最常见的遗传性凝血因子缺乏的疾病,包括血友病A(血友病球蛋白缺乏症,AHG缺乏症,第Ⅷ因子缺乏症),血友病B(血浆凝血活酶成份缺乏症,PTC缺乏症,第Ⅸ因子缺乏症)和血友病C(血浆凝血活酶前质缺乏症,PTA缺乏症,第Ⅺ因子缺乏症)。本病因严重出血危及生命或反复关节出血致残。因此,必须对血友病的出血采取紧急处理。临床表现全身各部位均可出现自发或轻度损伤后的程度不等的出血。如发生渗血可持继数小时、数天、数周之久。出血部位:1.粘膜:算衄、牙龈出血,舌尖破损出血。2.自发或外伤后皮下或肌肉血肿:多见于阴囊、大腿和臀部。3.关节出血:见于重型和中型患者,最常见于膝、踝和肘,次为髋、 Hemophilia is the most common hereditary factor deficiency, including hemophilia A (hemophilia globulin deficiency, AHG deficiency, factor VIII deficiency), hemophilia B (plasma thromboplastin component Deficiency, PTC deficiency, factor IX deficiency) and hemophilia C (prothrombocytopenia, PTA deficiency, factor XI deficiency). The cause of severe bleeding or life-threatening bleeding caused by repeated joint disability. Therefore, we must urgently deal with the bleeding of hemophilia. Clinical manifestations of various parts of the body may occur spontaneously or mildly varying degrees of bleeding after. If the occurrence of bleeding can sustain the number of hours, days, weeks long. Bleeding site: 1. Mucosa: count 算, bleeding gums, tongue bleeding. 2. Spontaneous or traumatic subcutaneous or muscle hematoma: more common in the scrotum, thighs and buttocks. 3. Joint bleeding: seen in heavy and medium-sized patients, the most common in the knee, ankle and elbow, followed by the hip,