纯词聋首先由Kussmaul于1877年描述,是一种少见的听语言理解障碍,主要特征是选择性听言语理解受损,而其它语言功能和阅读能力保留。对于其病理部位及发病机理长期以来还无统一认识。一个世纪以来国外文献报道不足百例,国内也鲜见。近来我们收治了1例两侧颞叶相继出血所致纯词聋,探讨其病理、发病机理及康复恢复过程。 Pure word deafness, first described by Kussmaul in 1877, is a rare obstruction of speech comprehension that is characterized by a selective impairment of speech comprehension, while retention of other language functions and reading ability. For its pathological location and pathogenesis for a long time there is no uniform understanding. Less than a hundred cases have been reported in foreign literature in a century, and there are few in China. Recently, we treated one case of bilateral temporal lobe hemorrhage caused by pure words deaf, discuss its pathology, pathogenesis and recovery process.