发作性运动源性舞蹈手足徐动症 (paroxysmalkinesigemicchoreoathetosis ,PKC)是一种少见的神经系统疾病 ,虽然 194 0年Mount和Reback开始对本病进行报道 ,但只是近 10多年才有较深入研究。国内周祥琴于2 0 0 0年首次报告 16例[1] ,随后又有 3篇相关报道[2～ 4 ] 。目前 ,对PKC Paroxysmal kinesium microchips (PKC) is a rare neurological disease. Although Mount and Reback began to report this disease in 1904, it was only in the past 10 years that more studies were conducted. Domestic Zhou Xiangqin first reported 16 cases in 2001 [1], followed by 3 related reports [2 ~ 4]. At present, to PKC