基底细胞痣综合征(BCNS)是一种罕见的、有遗传倾向的皮肤及其它器官的疾病,为常染色体显性遗传。BCNS患者的基底细胞上皮瘤(BCEs)皮损通常数目多、范围广,且终生发展。 本文报告1例58岁的男性患者,10年间在其胸、腹、背、腰部逐渐出现大小、形态不一,正常肤色或黑色斑片和斑块表面粗糙。在腰部,肿瘤数目众多,且大多数融合,形成约15cm×20cm的大片损害,另有一直径约1cm的半球形 Basal cell nevus syndrome (BCNS) is a rare, genetically predisposed skin and other organ disease that is autosomal dominant. The basal cell epithelial tumors (BCEs) in patients with BCNS usually have a large number of lesions, a wide range, and a lifetime of development. This article reports a case of a 58-year-old male patient who, in the 10 years, gradually appeared on the chest, abdomen, back, and waist in size, shape, and normal skin color or black patches and plaque surface roughness. At the waist, a large number of tumors, and most of the fusion, formed a large lesion of about 15cm x 20cm, and a hemispherical diameter of about 1cm