小儿多囊肾又称常染色体隐性遗传性多囊肾 (ＡＲＰＫＤ) ,国外报道很少 ,国内罕见报道。现将我院 1992～ 1998年收治的 10例报告如下。一般资料 :本文 10例中男 6例 ,女4例。确诊年龄 7天至 11岁 (中位数 7岁 )。此 10例的父母均非近亲结婚。 10例中 3例有家族史 :例 6的父母及 Polycystic kidney disease in children, also known as autosomal recessive hereditary polycystic kidney disease (ARPKD), few foreign reports, rare domestic reports. Now our hospital from 1992 to 1998 admitted 10 cases are as follows. General information: This article 10 cases in 6 males and 4 females. The diagnosed age ranged from 7 days to 11 years (median 7 years). All 10 parents were not married. Three of the 10 patients had a family history of: 6 cases of parents and